With approximately 150 cases reported to date, congenital erythropoietic porphyria (CEP) is an extremely rare, autosomal recessively inherited condition. In few cases this deficiency leads to deposition of red-brown pigments in the teeth. This case report described the microscopic study of the extracted tooth sample along with preventive, restorative dental management and oral health counseling in a rare case of Congenital Erythropoietic Porphyria.
Key words: Erythropoietic porphyria, oral health, pigmentation.

Corresponding author: Dr Prachi Sijeria, Senior Lecturer, Department of Pediatric and Preventive Dentistry, Rishiraj College of Dental Sciences and Research Centre Bhopal, M.P., India

This article may be cited as: Sijeria P, Bhartia R, Sahu T, Shrivastav R, KV Swamy  N, Kulkarni S. The dental management of paediatric patient with congenital erythropoietic porphyria. Int J Res Health Allied Sci 2017;3(4):31-34.