Ameloblast carcinoma is a rare tumor of the facial bones with features of ameloblastoma and carcinoma. It occurs more frequently in the mandible than in the maxilla. Surgical resection with 2–3 cm bone margins, is the current modality for the treatment of AC. Postoperative Radiotherapy may be beneficial who have locally recurred or those with residual disease after resection. The prognosis of AC is poor. The recurrent rate was 50%–90%, whereas the metastatic rate has been reported about 30%.